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Benign chronic familial pemphigus

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Benign chronic familial pemphigus

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29.10.2012 • Sonuncu dəyişiklik 01.01.2000
Duodecim Medical Publications Ltd

Benign chronic familial pemphigus (Morbus Hailey-Hailey) at the level of the lower ribs. A young lady noticed these first symptoms of a chronic disease only in adulthood. Therapy with topical corticoids of medium potency was successful in a couple of weeks. Morbus Darier (dyskeratosis congenita) is the main differential diagnosis.

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